DILATATION DES BRONCHES REVELANT UN SYNDROME DE KARTAGENER : A PROPOS DUN CAS ET REVUE DE LA LITTERATURE

Primary ciliary dyskinesias (PCD) are rare genetic diseases with autosomal recessive transmission, affecting nearly 1/15000 births, due to a structural/functional defect of cilia. Kartagener syndrome (KS) represents 50% PCDs and is characterised by the triad bronchiectasis, chronic sinusitis situs inversus. It manifested clinical signs upper lower respiratory infections or infertility. Situs inversus often discovered incidentally. The diagnosis confirmed specialized centers based on analysis ultrastructure electron microscopy beats light microscopy/high speed video , measurement nasal nitric oxide flow tests. Treatment supportive in line recommendations for management cystic fibrosis idiopathic adult bronchiectasies. includes physiotherapy, antibiotic medication treat infections, vaccinations local treatment otorhinolaryngeal tract if necessary. We present here case 23-year-old woman history recurrent since her early age, who consulted cough, bronchorrhea dyspnea. evolution failure slowed exacerbations.